Quelle est la prévalence des Hémochromatoses de type 1?

Combien de personnes affecte les Hémochromatoses de type 1? Est-ce que cela a la même prévalence chez les hommes et les femmes ? Et dans les différents pays ?

Original


Its prevalence is estimated to be 3–5/1000 in Caucasians. A single mutation, C282Y in the HFE gene explains 80–90% of all diagnosed cases in populations of northwestern European ancestry. The importance of another frequent mutation in this gene, H63D, as well as of C282Y/H63D compound heterozygotes, is still a matter of debate

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