Moyamoya disease is a rare cerebrovascular disorder characterized by the narrowing or blockage of the major blood vessels in the brain. It primarily affects the arteries at the base of the brain, leading to reduced blood flow and an increased risk of stroke.
The prevalence of Moyamoya varies across different populations and regions. In Japan, where the condition was first identified, it is estimated to affect approximately 1 in every 100,000 individuals. However, the prevalence is lower in other parts of the world, such as Europe and North America, where it is estimated to be around 0.086 to 0.35 cases per 100,000 individuals.
Moyamoya has a higher prevalence in certain ethnic groups, particularly individuals of Asian descent, including Japanese, Korean, and Chinese populations. In these groups, the prevalence can be as high as 10 to 100 times greater than in other populations.
While Moyamoya is considered a rare condition, it is important to note that the prevalence may be underestimated due to underdiagnosis or misdiagnosis. Early detection and proper management are crucial in improving outcomes for individuals with Moyamoya disease.