Short answer · Medically reviewed summary · Last updated: 2026-05-08
Churg Strauss Syndrome, now clinically known as Eosinophilic Granulomatosis with Polyangiitis (EGPA), is classified under the ICD-10 code M30.1 (Polyarteritis with lung involvement). In the older ICD-9 coding system, this condition was identified by the code 446.4. What exactly is Churg Strauss Syndrome? Churg Strauss Syndrome is a rare systemic necrotizing vasculitis characterized by asthma, peripheral blood eosinophilia, and inflammation of the blood vessels.
ICD10 code of Churg Strauss Syndrome and ICD9 code
ICD-10 and ICD-9 codes for Churg Strauss Syndrome, with classification details for clinicians, coders and patients.
Churg Strauss Syndrome, now clinically known as Eosinophilic Granulomatosis with Polyangiitis (EGPA), is classified under the ICD-10 code M30.1 (Polyarteritis with lung involvement). In the older ICD-9 coding system, this condition was identified by the code 446.4.
What exactly is Churg Strauss Syndrome?
Churg Strauss Syndrome is a rare systemic necrotizing vasculitis characterized by asthma, peripheral blood eosinophilia, and inflammation of the blood vessels. Because Churg Strauss Syndrome affects multiple organ systems, including the lungs, skin, nerves, and heart, accurate coding is essential for insurance documentation and tracking clinical outcomes within the 126-member community at DiseaseMaps.org.
Why did the name change from Churg Strauss Syndrome?
While many patients still use the term Churg Strauss Syndrome, the medical community adopted the name Eosinophilic Granulomatosis with Polyangiitis (EGPA) to better reflect the underlying pathology of the disease. Despite this change in nomenclature, the ICD-10 code M30.1 remains the standard identifier for Churg Strauss Syndrome in clinical and administrative settings worldwide.
How is the condition documented in medical records?
Medical coding for Churg Strauss Syndrome typically involves the following considerations:
- ICD-10 M30.1: The primary diagnostic code for polyarteritis with lung involvement (EGPA).
- ICD-9 446.4: The historical code used prior to the global transition to ICD-10.
- Comorbidity Coding: Physicians often supplement these codes with additional identifiers for asthma (J45) or eosinophilia (D72.1) to provide a complete clinical picture.
Next steps
- Confirm your specific diagnostic coding with your rheumatologist or immunologist during your next appointment.
- Connect with the 126 members at DiseaseMaps.org who are navigating life with Churg Strauss Syndrome to share experiences.
- Keep a personal health record binder containing your diagnostic history and relevant ICD codes for specialists.
Medical disclaimer: This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment; always consult with a qualified healthcare provider regarding your specific health needs.
References
- NIH Genetic and Rare Diseases Information Center (GARD): Eosinophilic granulomatosis with polyangiitis.
- Orphanet: Eosinophilic granulomatosis with polyangiitis (ORPHA:139).
- Vasculitis Foundation: Patient resources for EGPA/Churg-Strauss.
- OMIM (Online Mendelian Inheritance in Man): Clinical synopsis for EGPA.
