Short answer · Medically reviewed summary · Last updated: 2026-05-08
Eales disease is classified under the ICD-10 code H35.09 (Other intraretinal microvascular abnormalities) and the ICD-9 code 362.18 (Retinal vasculitis). Because it is a rare idiopathic retinal vasculitis, it does not have a unique, disease-specific diagnostic code in either system, necessitating the use of these broader ophthalmological classifications. What is the clinical nature of Eales disease? Eales disease is a rare, idiopathic inflammatory condition primarily affecting the peripheral retina.
ICD10 code of Eales Disease and ICD9 code
ICD-10 and ICD-9 codes for Eales Disease, with classification details for clinicians, coders and patients.
Eales disease is classified under the ICD-10 code H35.09 (Other intraretinal microvascular abnormalities) and the ICD-9 code 362.18 (Retinal vasculitis). Because it is a rare idiopathic retinal vasculitis, it does not have a unique, disease-specific diagnostic code in either system, necessitating the use of these broader ophthalmological classifications.
What is the clinical nature of Eales disease?
Eales disease is a rare, idiopathic inflammatory condition primarily affecting the peripheral retina. It is characterized by three distinct stages: periphlebitis, capillary non-perfusion, and neovascularization. Patients with Eales disease often present with symptoms like floaters, blurred vision, or sudden vision loss due to vitreous hemorrhage. Within the DiseaseMaps community, 23 people have shared their experiences with Eales disease, highlighting the emotional toll of navigating a condition that often lacks a single, definitive diagnostic code.
How is Eales disease diagnosed and classified?
Diagnosis of Eales disease is typically one of exclusion, meaning other systemic inflammatory or infectious diseases must be ruled out first. Since there is no specific ICD code for Eales disease, clinicians rely on clinical presentation and imaging to track the progression of the condition. Key clinical features include:
- Peripheral retinal periphlebitis (inflammation of the retinal veins)
- Peripheral retinal ischemia (lack of blood flow)
- Neovascularization of the retina or optic disc
- Recurrent vitreous hemorrhages
Is there a known cause for Eales disease?
The exact etiology of Eales disease remains unknown, though it is strongly associated with a hypersensitivity reaction to tuberculoproteins. While Eales disease is not strictly considered hereditary, the underlying immunological triggers are a subject of ongoing research. Because Eales disease primarily affects young, healthy males, it is essential to monitor for systemic health markers during the diagnostic process.
Next steps
- Consult a retina specialist or uveitis expert for a comprehensive dilated fundus examination.
- Undergo fluorescein angiography to map the extent of retinal vascular involvement in Eales disease.
- Join the 23-member strong community at DiseaseMaps.org to share experiences and coping strategies with others living with Eales disease.
Medical disclaimer: This content is for educational purposes only and does not constitute professional medical advice, diagnosis, or treatment; always seek the guidance of your physician regarding a medical condition.
References
- National Institutes of Health (NIH) - Genetic and Rare Diseases Information Center (GARD)
- Orphanet: Portal for rare diseases and orphan drugs
- PubMed: Clinical reviews on idiopathic retinal vasculitis
- International Classification of Diseases (ICD-10/ICD-9) coding manuals
