¿Cuál es la historia de la Hemocromatosis Hereditaria?

Historia de Hemocromatosis Hereditaria: cuándo y cómo se descubrió, y los hitos de su investigación desde entonces.

Original


The disease was first described in 1865 by Armand Trousseau in a report on diabetes in patients presenting with a bronze pigmentation of their skin. Trousseau did not associate diabetes with iron accumulation; the recognition that infiltration of the pancreas with iron might disrupt endocrine function resulting in diabetes was made by Friedrich Daniel von Recklinghausen in 1890

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