I'm a 38 year old male with erythomelalgia disease and hypohidrosis caused by Fabry Disease and I have Chronic Kidney Disease so the following diet addresses both Fabry and CKD so if you don't have CKD you don't need to be as strict with protein or minerals. I have found a reduction in both severity and frequency of burning (erythomelalgia) using various versions of this diet. A Fabry diet, in my opinion, is one where the chemical bonds in the food don't join fats and carbs because Fabry Disease means the person can't break this bond because they either don't have, don't have enough or the Alph-galactosidase enzymes they do have are improperly folded. A CKD diet means it is low in protein and minerals, particularly sodium (salt), potassium, and phosphorus.
*This diet does contain some fat-carb bonds (ex. walnuts). In order to consume this 1/3 cup of walnuts I eat 5 Beano pills (Walmart and Target have their own brand for this pill). This pill, as far as I know, is the enzyme my body needs to break this fat-carb bond.
*If I want to eat off diet I compare the fat and carbs on the nutrition label and whichever is lower I consume 1 Beano pill per gram. If the nutrition label is unavailable I eat 1 pill per bite but Warning: too much Beano (2 pills per bite) has given me an upset stomach and diarrhea while not enough can cause a continuation of nerve damage which causes my erythomelalgia disease and hypohidrosis, so clearly it is better to eat based on the nutrition label.
Example Fabry/CKD Diet: a place to start
Breakfast: Eggs with onion powder, garlic powder, cracked black pepper, and low sodium ketchup.
1st Snack: 1/3 cup walnuts with 5 Beano pills
Drink: flavored sparkling water
1st Lunch: 1 cup steamed white rice, 1 tablespoon extra virgin olive oil, 1 tablespoon balsamic vinegar, onion powder, low sodium ketchup, curry powder (for flavor)
1st Dessert: 1/2 cup pears in juice with 2 tablespoons of benefiber (or store equivalent)
2nd Snack: 1/3 cup almonds with 1 Beano for every 3 almonds
2nd Lunch: 1 cup steamed white rice, 1 tablespoon extra virgin olive oil, 1 tablespoon balsamic vinegar, onion powder, low sodium ketchup, curry powder (for flavor)
2nd Dessert: cherry pie filling (1/3 cup)
Dinner: 1/3 cup walnuts with 5 Beano pills
Vitamins:
K-2 100 mg (1 pill per day)
Vitamin A 2500 mg (1 pill per week)
ProRenal + D, Multivitamin with Omega 3 (2 pills per day)
Vitamin C 250 mg (1 pill per week)
Vitamin D 1000 IU (1 pill per day)
*I switch pie filling and fruit deserts to make the diet more interesting.
*I switch EVOO for Mayo sometimes (read the label to ensure it has no carbs and is low sodium)
*Eat Beano before eating food requiring Beano. Warning: Beano nor any equivalent have endorsed these statements nor have there been any tests, to the authors knowledge, to prove or disprove these claims.
*Results should be a direct relationship with how strictly you follow these guidelines (this diet) so the primary aspect of success to living with Fabry Disease is self control / discipline.
*References:
https://cronometer.com
https://nutritionfacts.org
https://nutritiondata.self.com
Warning: the information provided is anecdotal and has not been evaluated by a doctor. Individual results may vary. Please consult with your physician(s) prior trying any thing mentioned.