Short answer · Medically reviewed summary · Last updated: 2026-05-08

Kawasaki Disease is officially known by its eponym, named after the Japanese pediatrician Tomisaku Kawasaki who first described it in 1967. While it is occasionally referred to as Mucocutaneous Lymph Node Syndrome, "Kawasaki Disease" remains the preferred clinical term used by medical professionals worldwide to ensure clear communication and accurate diagnosis. What are the historical and alternative names for Kawasaki Disease? Historically, Kawasaki Disease was identified as a distinct entity based on its clinical presentation of fever, rash, and lymphadenopathy.

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Kawasaki Disease synonyms

Other names for Kawasaki Disease: synonyms, acronyms and related terms used by doctors and patients.

Kawasaki Disease is also known as...

Kawasaki Disease is officially known by its eponym, named after the Japanese pediatrician Tomisaku Kawasaki who first described it in 1967. While it is occasionally referred to as Mucocutaneous Lymph Node Syndrome, "Kawasaki Disease" remains the preferred clinical term used by medical professionals worldwide to ensure clear communication and accurate diagnosis.



What are the historical and alternative names for Kawasaki Disease?


Historically, Kawasaki Disease was identified as a distinct entity based on its clinical presentation of fever, rash, and lymphadenopathy. Before the medical community settled on the eponymous title, it was most commonly referred to as Mucocutaneous Lymph Node Syndrome. This descriptive name highlights the primary areas of inflammation: the mucous membranes, the skin, and the lymph nodes. In older medical literature or specific regional texts, you may occasionally see it referenced as infantile polyarteritis nodosa, though this term is now considered imprecise and is rarely used in contemporary practice.



Why does Kawasaki Disease have multiple names?


The variety of names for Kawasaki Disease stems from the evolution of medical diagnostics and the transition from descriptive terminology to eponymous recognition.


  • Mucocutaneous Lymph Node Syndrome: A descriptive label focusing on the hallmark symptoms.

  • Kawasaki Disease: The standard clinical identifier honoring Dr. Tomisaku Kawasaki.

  • KD: The standard medical abbreviation used in hospital records and clinical research.

  • Infantile Polyarteritis Nodosa: An outdated, historical term occasionally found in archives.



How is Kawasaki Disease classified in medical systems?


In global medical registries, Kawasaki Disease is categorized under specific codes to facilitate research and insurance billing. It is listed as ORPHA:480 in the Orphanet database and has a dedicated entry in the OMIM (Online Mendelian Inheritance in Man) database as #611775. The ICD-10 code for Kawasaki Disease is M30.3, which confirms its classification as a form of systemic vasculitis.



Next steps



  • Consult a pediatric rheumatologist or cardiologist if you suspect symptoms of Kawasaki Disease.

  • Connect with the 351 members of our DiseaseMaps.org community to share experiences and coping strategies.

  • Review diagnostic criteria provided by the American Heart Association (AHA) to understand the clinical standard of care.



Medical disclaimer: This information is for educational purposes and does not replace professional medical advice, diagnosis, or treatment.



References



  • Orphanet (ORPHA:480)

  • NIH Genetic and Rare Diseases Information Center (GARD)

  • OMIM (Online Mendelian Inheritance in Man, #611775)

  • American Heart Association (AHA) - Kawasaki Disease Guidelines

Author: DiseaseMaps Editorial Team
Reviewed against authoritative medical sources (NIH GARD, Orphanet, OMIM)
Last updated: 2026-05-08
Sources cited: Orphanet (ORPHA:480) · NIH Genetic and Rare Diseases Information Center (GARD) · OMIM (Online Mendelian Inheritance in Man, #611775) · American Heart Association (AHA) - Kawasaki Disease Guidelines · WHO
Medical disclaimer: This information does not substitute professional medical advice. Always consult your doctor before making health decisions.
Source: DiseaseMaps.org
2 answers
Some other names are just Kawasaki, KD and mucocutaneous lymph node syndrome

Posted Jun 15, 2018 by brittanyh664 1350

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