Short answer · Medically reviewed summary · Last updated: 2026-05-08
Lipomyelomeningocele is classified under the ICD-10 code Q05.4 (unspecified spina bifida with hydrocephalus) or more specifically Q05.2 (lumbar spina bifida with hydrocephalus), though it is frequently coded under Q05.7 (thoracic spina bifida) depending on the anatomical level. In the legacy ICD-9-CM system, Lipomyelomeningocele was typically categorized under 741.0 (spina bifida with hydrocephalus) or 741.9 (spina bifida without hydrocephalus). What is the clinical nature of Lipomyelomeningocele? Lipomyelomeningocele is a form of closed neural tube defect characterized by a lipoma (fatty mass) that extends through a defect in the vertebral column to attach to the spinal cord.
ICD10 code of Lipomyelomeningocele and ICD9 code
ICD-10 and ICD-9 codes for Lipomyelomeningocele, with classification details for clinicians, coders and patients.
Lipomyelomeningocele is classified under the ICD-10 code Q05.4 (unspecified spina bifida with hydrocephalus) or more specifically Q05.2 (lumbar spina bifida with hydrocephalus), though it is frequently coded under Q05.7 (thoracic spina bifida) depending on the anatomical level. In the legacy ICD-9-CM system, Lipomyelomeningocele was typically categorized under 741.0 (spina bifida with hydrocephalus) or 741.9 (spina bifida without hydrocephalus).
What is the clinical nature of Lipomyelomeningocele?
Lipomyelomeningocele is a form of closed neural tube defect characterized by a lipoma (fatty mass) that extends through a defect in the vertebral column to attach to the spinal cord. Unlike open spina bifida, the spinal cord in Lipomyelomeningocele is covered by skin, which often masks the underlying tethered cord syndrome. At DiseaseMaps.org, 40 members are currently navigating the complexities of this diagnosis, highlighting the importance of specialized neurosurgical monitoring.
How is Lipomyelomeningocele classified for medical billing?
Because Lipomyelomeningocele is a complex malformation, diagnostic coding often depends on the presence of associated anomalies. Common codes include:
- ICD-10-CM: Q05.2 (Lumbar spina bifida with hydrocephalus) or Q05.7 (Thoracic spina bifida without hydrocephalus).
- ICD-9-CM: 741.0x (Spina bifida with hydrocephalus) or 741.9x (Spina bifida without hydrocephalus).
- Clinical Note: Physicians often utilize additional codes to describe specific neurological deficits, such as neurogenic bladder (N31.9) or gait abnormalities (R26.89).
Is Lipomyelomeningocele hereditary?
Most cases of Lipomyelomeningocele occur sporadically, meaning there is no clear family history. While the exact cause remains multifactorial—involving both genetic predispositions and environmental factors—it is not considered a classic Mendelian inherited disorder. Genetic counseling is recommended to discuss recurrence risks, which are generally low but require careful clinical evaluation.
Next steps
- Consult a pediatric neurosurgeon to monitor for tethered cord progression.
- Request a baseline MRI of the entire spine to evaluate the extent of the Lipomyelomeningocele.
- Connect with the 40 members on DiseaseMaps.org to share experiences regarding symptom management.
- Schedule regular urological evaluations to monitor for potential neurogenic bladder.
Medical disclaimer: This information is for educational purposes only and should not replace professional medical advice, diagnosis, or treatment from a qualified healthcare provider.
References
- NIH Genetic and Rare Diseases Information Center (GARD): Lipomyelomeningocele
- Orphanet: Spinal dysraphism
- OMIM (Online Mendelian Inheritance in Man): Spina Bifida entry #182940
- International Classification of Diseases, 10th Revision (ICD-10) Browser
