Short answer · Medically reviewed summary · Last updated: 2026-05-08
Palmoplantar Keratoderma is primarily classified under ICD-10 code L85.1 (Acquired keratosis [keratoderma] palmaris et plantaris) or Q82.8 (Other specified congenital malformations of skin) for hereditary forms, while the legacy ICD-9 code is 701.1. Because Palmoplantar Keratoderma encompasses a broad spectrum of clinical presentations, the specific code used depends on whether the condition is inherited (genodermatosis) or acquired. How is Palmoplantar Keratoderma classified in medical coding? Medical coding for Palmoplantar Keratoderma is complex because it is not a single disease, but a heterogeneous group of disorders characterized by hyperkeratosis of the palms and soles.
ICD10 code of Palmoplantar Keratoderma and ICD9 code
ICD-10 and ICD-9 codes for Palmoplantar Keratoderma, with classification details for clinicians, coders and patients.
Palmoplantar Keratoderma is primarily classified under ICD-10 code L85.1 (Acquired keratosis [keratoderma] palmaris et plantaris) or Q82.8 (Other specified congenital malformations of skin) for hereditary forms, while the legacy ICD-9 code is 701.1. Because Palmoplantar Keratoderma encompasses a broad spectrum of clinical presentations, the specific code used depends on whether the condition is inherited (genodermatosis) or acquired.
How is Palmoplantar Keratoderma classified in medical coding?
Medical coding for Palmoplantar Keratoderma is complex because it is not a single disease, but a heterogeneous group of disorders characterized by hyperkeratosis of the palms and soles. ICD-10-CM provides code L85.1 for non-hereditary forms, while hereditary variants are often coded under Q82.8. Practitioners must differentiate between the diffuse, focal, and punctate patterns of Palmoplantar Keratoderma to ensure accurate billing and clinical documentation.
What are the common clinical patterns of this condition?
Palmoplantar Keratoderma manifests through various morphological patterns. Clinicians categorize these based on the distribution of skin thickening:
- Diffuse: Characterized by a uniform, marble-like thickening of the entire palm and sole surface.
- Focal: Thickening typically occurs at sites of chronic friction or pressure (e.g., heels, ball of the foot).
- Punctate: Displays multiple small, seed-like keratotic papules across the palms and soles.
- Striate: Presents as linear bands of hyperkeratosis, often following the longitudinal axis of the digits.
Is Palmoplantar Keratoderma hereditary?
Many forms of Palmoplantar Keratoderma are genetic, following autosomal dominant or autosomal recessive inheritance patterns. Mutations in genes such as KRT1, KRT9, or GJB2 are frequently identified in affected families. Understanding the genetic basis is vital, as some forms of Palmoplantar Keratoderma may be associated with systemic findings, such as deafness or esophageal cancer risk, requiring multidisciplinary monitoring.
Next steps
- Consult a board-certified dermatologist to confirm your specific subtype through clinical evaluation or genetic testing.
- Connect with the 12 members of our DiseaseMaps.org community to share experiences on daily skin management.
- Request a referral to a genetic counselor if you suspect a hereditary form of the condition.
Medical disclaimer: This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment; always seek the advice of your physician or other qualified health provider.
References
- NIH Genetic and Rare Diseases Information Center (GARD): Palmoplantar Keratoderma
- Orphanet: Rare diseases database for keratoderma
- OMIM (Online Mendelian Inheritance in Man): Registry of genetic variants associated with keratoderma
- ICD-10 Data: L85.1 Acquired keratosis palmaris et plantaris
