Short answer · Medically reviewed summary · Last updated: 2026-05-08

The primary ICD-10 code for Polyarteritis Nodosa is M30.0, while the legacy ICD-9 code is 446.0. These codes are used globally by healthcare providers and insurance systems to categorize this rare, systemic necrotizing vasculitis that affects medium-sized arteries. What is the clinical significance of the Polyarteritis Nodosa classification? Polyarteritis Nodosa is a serious condition characterized by inflammation of the vessel walls, leading to ischemia and organ damage.

1 people with Polyarteritis Nodosa have shared their first-person experience on this question at DiseaseMaps.

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ICD10 code of Polyarteritis Nodosa and ICD9 code

ICD-10 and ICD-9 codes for Polyarteritis Nodosa, with classification details for clinicians, coders and patients.

ICD9 and ICD10 codes of Polyarteritis Nodosa

The primary ICD-10 code for Polyarteritis Nodosa is M30.0, while the legacy ICD-9 code is 446.0. These codes are used globally by healthcare providers and insurance systems to categorize this rare, systemic necrotizing vasculitis that affects medium-sized arteries.



What is the clinical significance of the Polyarteritis Nodosa classification?


Polyarteritis Nodosa is a serious condition characterized by inflammation of the vessel walls, leading to ischemia and organ damage. Because Polyarteritis Nodosa can affect multiple organ systems—including the kidneys, skin, nerves, and gastrointestinal tract—accurate diagnostic coding using M30.0 is essential for coordinating multidisciplinary care across various medical specialties.



How is a diagnosis of Polyarteritis Nodosa confirmed?


Clinicians do not rely on codes alone; rather, they utilize a combination of clinical, laboratory, and imaging findings. Diagnosis of Polyarteritis Nodosa typically involves identifying characteristic "beading" on angiography or confirming necrotizing vasculitis through tissue biopsy. Our DiseaseMaps community, which currently includes 57 individuals living with Polyarteritis Nodosa, emphasizes that early diagnosis is vital for managing the systemic nature of the disease.



What are the key diagnostic criteria for Polyarteritis Nodosa?


To assist in recognizing the disease, the American College of Rheumatology established criteria for identifying Polyarteritis Nodosa. These include:



  • Weight loss greater than or equal to 4 kg.

  • Livedo reticularis (mottled skin discoloration).

  • Testicular pain or tenderness.

  • Myalgia, weakness, or leg tenderness.

  • Mono- or polyneuropathy.

  • Diastolic blood pressure greater than 90 mmHg.

  • Elevated blood urea nitrogen or creatinine levels.

  • Presence of Hepatitis B surface antigen or antibody.



Is Polyarteritis Nodosa considered a chronic condition?


Yes, Polyarteritis Nodosa is a chronic, often relapsing disease that requires long-term management. While the ICD-10 code M30.0 helps track the condition, the real-world experience of those with Polyarteritis Nodosa involves navigating complex treatment regimens, often including corticosteroids and immunosuppressive therapies to induce and maintain remission.



Next steps



  • Consult with a board-certified rheumatologist to discuss your specific symptoms and diagnostic codes.

  • Connect with the 57 members of the DiseaseMaps community to share experiences and coping strategies.

  • Maintain a detailed symptom log to assist your medical team in evaluating treatment effectiveness.



Medical disclaimer: This information is for educational purposes only and does not replace professional medical advice, diagnosis, or treatment.



References



  • NIH Genetic and Rare Diseases Information Center (GARD): Polyarteritis Nodosa

  • Orphanet: ORPHA683 (Polyarteritis Nodosa)

  • OMIM: Entry 610058 (Polyarteritis Nodosa)

  • American College of Rheumatology: Vasculitis Clinical Guidelines

Author: DiseaseMaps Editorial Team
Reviewed against authoritative medical sources (NIH GARD, Orphanet, OMIM)
Last updated: 2026-05-08
Medical disclaimer: This information does not substitute professional medical advice. Always consult your doctor before making health decisions.
Source: DiseaseMaps.org
2 answers
They are billable medical codes used for reimbursement claims.

Posted Mar 31, 2018 by Verna 3000

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This is my story about Polyarthritis Nodosa, sorry in advance for my poor english or grammar, it is not my first language. When I was young, I was an active child that is into sports, biking, running, and overall playing. I was also the type of c...

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