Short answer · Medically reviewed summary · Last updated: 2026-05-08
The primary ICD-10 code for Vestibular Schwannoma, also known as acoustic neuroma, is D33.3 (Benign neoplasm of cranial nerves). In the older ICD-9-CM classification system, this condition was coded as 225.1 (Benign neoplasm of cranial nerves). What is Vestibular Schwannoma-Acoustic neuroma? A Vestibular Schwannoma-Acoustic neuroma is a rare, non-cancerous (benign) tumor that grows on the vestibular nerve, which connects the inner ear to the brain.
ICD10 code of Vestibular Schwannoma-Acoustic neuroma and ICD9 code
ICD-10 and ICD-9 codes for Vestibular Schwannoma-Acoustic neuroma, with classification details for clinicians, coders and patients.
The primary ICD-10 code for Vestibular Schwannoma, also known as acoustic neuroma, is D33.3 (Benign neoplasm of cranial nerves). In the older ICD-9-CM classification system, this condition was coded as 225.1 (Benign neoplasm of cranial nerves).
What is Vestibular Schwannoma-Acoustic neuroma?
A Vestibular Schwannoma-Acoustic neuroma is a rare, non-cancerous (benign) tumor that grows on the vestibular nerve, which connects the inner ear to the brain. Because this tumor grows on the nerve responsible for balance and hearing, a Vestibular Schwannoma-Acoustic neuroma can lead to significant sensory changes. While they do not spread to other parts of the body, their location near vital brain structures makes precise diagnosis and monitoring essential.
How are ICD codes used for Vestibular Schwannoma-Acoustic neuroma?
Medical billing and diagnostic coding for a Vestibular Schwannoma-Acoustic neuroma are critical for ensuring accurate health records and insurance coverage. While D33.3 is the standard code, your medical team may also use additional codes to document specific symptoms or complications associated with your Vestibular Schwannoma-Acoustic neuroma, such as:
- H90.3: Sensorineural hearing loss, bilateral
- H81.0: Meniere's disease (or related balance disorders)
- R42: Dizziness and giddiness
Is Vestibular Schwannoma-Acoustic neuroma hereditary?
Most cases of Vestibular Schwannoma-Acoustic neuroma occur sporadically. However, if an individual develops bilateral tumors (tumors on both sides), it is often a clinical sign of Neurofibromatosis type 2 (NF2), a hereditary condition. Genetic counseling is recommended for patients diagnosed with Vestibular Schwannoma-Acoustic neuroma at a young age or those with a family history of the condition.
Next steps
- Consult with a neurotologist or neurosurgeon who specializes in the management of Vestibular Schwannoma-Acoustic neuroma.
- Connect with the 41 members currently sharing their experiences with Vestibular Schwannoma-Acoustic neuroma on DiseaseMaps.org to find peer support.
- Request a copy of your MRI imaging reports to understand the size and growth rate of your tumor.
Medical disclaimer: This content is for informational purposes only and does not constitute professional medical advice, diagnosis, or treatment; always seek the advice of your physician regarding a medical condition.
References
- NIH Genetic and Rare Diseases Information Center (GARD): Vestibular Schwannoma
- Orphanet: Rare Disease Database (ORPHA: 792)
- World Health Organization: International Classification of Diseases (ICD-10)
- Acoustic Neuroma Association: Patient resources and clinical guidelines
