Short answer · Medically reviewed summary · Last updated: 2026-04-07
The ICD-10 code for Takayasu’s arteritis is M31.4, while the corresponding ICD-9 code is 446.7. As a specialist who has worked with many patients navigating the complexities of Takayasu’s arteritis, I understand that these codes are more than just administrative labels; they are the keys to accessing specialized care, insurance coverage, and disability support. Takayasu’s arteritis is a rare form of large-vessel vasculitis that primarily affects the aorta and its major branches, often leading to stenosis, occlusion, or aneurysms.
3 people with Takayasus Arteritis have shared their first-person experience on this question at DiseaseMaps.
ICD10 code of Takayasus Arteritis and ICD9 code
ICD-10 and ICD-9 codes for Takayasus Arteritis, with classification details for clinicians, coders and patients.
The ICD-10 code for Takayasu’s arteritis is M31.4, while the corresponding ICD-9 code is 446.7.
As a specialist who has worked with many patients navigating the complexities of Takayasu’s arteritis, I understand that these codes are more than just administrative labels; they are the keys to accessing specialized care, insurance coverage, and disability support. Takayasu’s arteritis is a rare form of large-vessel vasculitis that primarily affects the aorta and its major branches, often leading to stenosis, occlusion, or aneurysms. Because it is a systemic inflammatory disease, accurate coding is essential for your medical team to coordinate multidisciplinary care between rheumatologists, vascular surgeons, and cardiologists.
Understanding Clinical Coding
In clinical practice, the ICD-10 code M31.4 (Aortic arch syndrome [Takayasu]) is used universally to identify Takayasu’s arteritis within electronic health records. While the ICD-9 system (code 446.7) has been largely retired in the United States in favor of ICD-10, you may still see it referenced in older medical records or historical research databases. Ensuring your medical chart reflects the correct diagnosis is vital, as Takayasu’s arteritis requires ongoing monitoring of blood pressure, pulses, and inflammatory markers like ESR and CRP.
Navigating the Journey
Living with Takayasu’s arteritis can feel overwhelming, especially when dealing with the administrative burden of healthcare. Please remember that your diagnosis is a tool for your care team to advocate for the targeted immunosuppressive therapies and surgical interventions you may require. If you are struggling with the emotional weight of this chronic condition, know that you are not alone; our community at DiseaseMaps.org provides a space to connect with others who truly understand the daily realities of managing this rare vascular disease. Always ensure your healthcare providers are aware of any new symptoms, as the progression of Takayasu’s arteritis can be insidious and requires vigilant, long-term follow-up.
Disclaimer: This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always seek the advice of your physician or other qualified health provider with any questions you may have regarding a medical condition.
References
- Orphanet: Takayasu arteritis (ORPHA:84)
- NIH Genetic and Rare Diseases Information Center (GARD): Takayasu arteritis
- OMIM (Online Mendelian Inheritance in Man): Takayasu Arteritis (Entry #222100)
446.6 ICD9
Posted May 31, 2017 by Salosh 3601
ICD9-446.7
Posted Sep 11, 2017 by Taylor 2650
CIE-10 es M31.4
Posted Sep 2, 2017 by Angie Cortéz 3550
