ICD10 code of Tethered Spinal Cord Syndrome and ICD9 code

Tethered Spinal Cord Syndrome is primarily classified under the ICD-10 code Q06.2 (Diastematomyelia) or Q06.1 (Hypoplasia and dysplasia of spinal cord), as there is no single specific code exclusively for tethered cord. In the legacy ICD-9-CM coding system, Tethered Spinal Cord Syndrome was most commonly reported using code 742.59 (Other specified anomalies of spinal cord).

What is Tethered Spinal Cord Syndrome?

Tethered Spinal Cord Syndrome is a neurological disorder caused by tissue attachments that limit the movement of the spinal cord within the spinal column. This abnormal attachment causes the spinal cord to stretch as a child grows or as the body moves, leading to potential nerve damage. While often associated with congenital conditions like spina bifida, Tethered Spinal Cord Syndrome can also occur in adults due to scarring from previous surgeries or trauma.

How is Tethered Spinal Cord Syndrome diagnosed?

Diagnosis of Tethered Spinal Cord Syndrome typically involves a combination of clinical evaluation and advanced imaging. Physicians look for specific dermatological markers on the lower back, such as dimples, tufts of hair, or hemangiomas, which may suggest an underlying tethering. The following diagnostic tools are essential:

• Magnetic Resonance Imaging (MRI): The gold standard for visualizing the conus medullaris and identifying the level of attachment.


• Urodynamic Testing: Used to evaluate bladder function, as urinary issues are often a primary symptom.


• Electromyography (EMG): Used to assess nerve conduction and muscle activity in the lower extremities.

Is Tethered Spinal Cord Syndrome hereditary?

Tethered Spinal Cord Syndrome is not strictly hereditary, though it is frequently associated with neural tube defects that have a multifactorial inheritance pattern. Many individuals with Tethered Spinal Cord Syndrome have no family history of the condition. In our DiseaseMaps community, 41 people with Tethered Spinal Cord Syndrome have shared their experiences, highlighting the diverse ways this diagnosis impacts patients of all ages.

Next steps

• Consult a pediatric or adult neurosurgeon specializing in spinal dysraphism.


• Maintain a symptom diary to track neurological changes, which is vital for surgical decision-making.


• Connect with the 41 members on DiseaseMaps.org to share experiences and coping strategies.

Medical disclaimer: This information is for educational purposes only and does not replace professional medical advice, diagnosis, or treatment.

References

• NIH Genetic and Rare Diseases Information Center (GARD): Tethered Spinal Cord Syndrome


• Orphanet: Rare disease database, ORPHA: 3244


• OMIM (Online Mendelian Inheritance in Man): Entry #601634


• World Health Organization: ICD-10 International Statistical Classification of Diseases