Short answer · Medically reviewed summary · Last updated: 2026-05-08
The primary ICD-10 code for Tetralogy of Fallot is Q21.3, while the historical ICD-9 code is 745.2. These classification codes are essential for medical billing, clinical documentation, and tracking the prevalence of Tetralogy of Fallot within healthcare systems globally. What is the clinical significance of Tetralogy of Fallot? Tetralogy of Fallot is a complex congenital heart defect characterized by four specific anatomical abnormalities: a ventricular septal defect, pulmonary stenosis, right ventricular hypertrophy, and an overriding aorta.
2 people with Tetralogy Of Fallot have shared their first-person experience on this question at DiseaseMaps.
ICD10 code of Tetralogy Of Fallot and ICD9 code
ICD-10 and ICD-9 codes for Tetralogy Of Fallot, with classification details for clinicians, coders and patients.
The primary ICD-10 code for Tetralogy of Fallot is Q21.3, while the historical ICD-9 code is 745.2. These classification codes are essential for medical billing, clinical documentation, and tracking the prevalence of Tetralogy of Fallot within healthcare systems globally.
What is the clinical significance of Tetralogy of Fallot?
Tetralogy of Fallot is a complex congenital heart defect characterized by four specific anatomical abnormalities: a ventricular septal defect, pulmonary stenosis, right ventricular hypertrophy, and an overriding aorta. Patients with Tetralogy of Fallot often experience cyanosis, commonly known as "blue baby syndrome," due to oxygen-poor blood circulating through the body. At DiseaseMaps.org, we support a community of 362 people with Tetralogy of Fallot who share their experiences navigating these structural heart challenges.
How are the ICD codes for Tetralogy of Fallot used?
Medical coding systems like ICD-10 and ICD-9 ensure that the diagnosis of Tetralogy of Fallot is standardized across clinical settings. These codes are vital for:
- Facilitating insurance authorization for cardiac surgeries and interventions.
- Allowing researchers to track the long-term outcomes of individuals living with Tetralogy of Fallot.
- Assisting hospitals in allocating specialized resources for pediatric cardiology departments.
Is Tetralogy of Fallot considered a hereditary condition?
While most cases of Tetralogy of Fallot occur sporadically, genetic factors can play a role. Approximately 15-20% of patients diagnosed with Tetralogy of Fallot may have an associated genetic syndrome, such as 22q11.2 deletion syndrome (DiGeorge syndrome). Genetic counseling is often recommended for families to understand the recurrence risks associated with Tetralogy of Fallot.
Next steps
- Consult a pediatric cardiologist or a congenital heart specialist to discuss your specific medical records and coding.
- Join the DiseaseMaps.org community to connect with 362 others who understand the journey of living with Tetralogy of Fallot.
- Request a referral to a genetic counselor if you have questions regarding the potential for recurrence in your family.
Medical disclaimer: This information is for educational purposes only and should not replace professional medical advice, diagnosis, or treatment.
References
- NIH Genetic and Rare Diseases Information Center (GARD): Tetralogy of Fallot overview.
- Orphanet (ORPHA:3337): Rare disease database entry for Tetralogy of Fallot.
- OMIM (Online Mendelian Inheritance in Man): Entry #187500 regarding the genetic architecture of Tetralogy of Fallot.
- World Health Organization (WHO): ICD-10 International Classification of Diseases.
Posted Feb 16, 2018 by Janco 3020
Posted Oct 5, 2017 by Morgane 2000
