Short answer · Medically reviewed summary · Last updated: 2026-05-08
Wallenberg syndrome, also known as lateral medullary syndrome, is classified under ICD-10 code I63.341 (Cerebral infarction due to thrombosis of the posterior inferior cerebellar artery) and historically under ICD-9 code 433.01. These codes are used for medical billing and clinical documentation to identify the specific vascular event that triggers this neurological condition. What is Wallenberg syndrome? Wallenberg syndrome is a rare neurological disorder caused by an infarction (stroke) in the lateral medulla of the brainstem.
ICD10 code of Wallenberg Syndrome and ICD9 code
ICD-10 and ICD-9 codes for Wallenberg Syndrome, with classification details for clinicians, coders and patients.
Wallenberg syndrome, also known as lateral medullary syndrome, is classified under ICD-10 code I63.341 (Cerebral infarction due to thrombosis of the posterior inferior cerebellar artery) and historically under ICD-9 code 433.01. These codes are used for medical billing and clinical documentation to identify the specific vascular event that triggers this neurological condition.
What is Wallenberg syndrome?
Wallenberg syndrome is a rare neurological disorder caused by an infarction (stroke) in the lateral medulla of the brainstem. This stroke typically results from an occlusion of the posterior inferior cerebellar artery or the vertebral artery. Because this area of the brain controls many autonomic and sensory functions, Wallenberg syndrome manifests with a distinct constellation of symptoms that can be life-altering for the 55 members of our DiseaseMaps.org community who live with this diagnosis.
How is Wallenberg syndrome diagnosed?
Diagnosis is primarily clinical, based on the sudden onset of characteristic neurological deficits, followed by confirmatory neuroimaging. Physicians look for the following clinical hallmarks of Wallenberg syndrome:
- Loss of pain and temperature sensation on the ipsilateral (same-sided) face and contralateral (opposite-sided) body.
- Vertigo and nystagmus, often accompanied by severe nausea and vomiting.
- Dysphagia and hoarseness caused by involvement of the nucleus ambiguus.
- Horner’s syndrome, characterized by a constricted pupil (miosis) and drooping eyelid (ptosis) on the affected side.
- Ataxia, presenting as a lack of voluntary coordination of muscle movements.
Is Wallenberg syndrome hereditary?
Wallenberg syndrome is not a genetic or hereditary condition. It is an acquired neurological event resulting from vascular compromise. While the stroke itself is not inherited, underlying risk factors such as hypertension, hyperlipidemia, or connective tissue disorders (like fibromuscular dysplasia) that may predispose an individual to arterial dissection or thrombosis can sometimes have a familial component.
Next steps
- Consult a vascular neurologist to manage secondary stroke prevention and long-term recovery.
- Engage with physical and speech therapists to address persistent ataxia and swallowing difficulties associated with Wallenberg syndrome.
- Join the DiseaseMaps.org community to connect with others who understand the unique recovery journey of Wallenberg syndrome.
Medical disclaimer: This information is for educational purposes only and does not constitute professional medical advice, diagnosis, or treatment; always seek the advice of your physician regarding a medical condition.
References
- NIH Genetic and Rare Diseases Information Center (GARD): Lateral Medullary Syndrome.
- Orphanet: Portal for rare diseases and orphan drugs (ORPHA: 3345).
- National Library of Medicine (PubMed): Clinical reviews on Wallenberg syndrome pathophysiology.
- American Heart Association/American Stroke Association: Guidelines for the prevention of stroke.
