Short answer · Medically reviewed summary · Last updated: 2026-05-08

The primary ICD-10 code for Arteriovenous Malformation (AVM) is Q27.3, specifically categorized under congenital peripheral arteriovenous malformations, while ICD-9 categorized these conditions under 747.6. Please note that specific coding may vary depending on the anatomical location of the Arteriovenous Malformation AVM, such as cerebral (Q28.2) or pulmonary (Q25.79) sites. What is the clinical significance of Arteriovenous Malformation AVM coding? Accurate coding for Arteriovenous Malformation AVM is essential for medical billing, insurance authorization for specialized imaging, and tracking clinical outcomes.

4 people with Arteriovenous Malformation AVM have shared their first-person experience on this question at DiseaseMaps.

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ICD10 code of Arteriovenous Malformation AVM and ICD9 code

ICD-10 and ICD-9 codes for Arteriovenous Malformation AVM, with classification details for clinicians, coders and patients.

ICD9 and ICD10 codes of Arteriovenous Malformation AVM

The primary ICD-10 code for Arteriovenous Malformation (AVM) is Q27.3, specifically categorized under congenital peripheral arteriovenous malformations, while ICD-9 categorized these conditions under 747.6. Please note that specific coding may vary depending on the anatomical location of the Arteriovenous Malformation AVM, such as cerebral (Q28.2) or pulmonary (Q25.79) sites.



What is the clinical significance of Arteriovenous Malformation AVM coding?


Accurate coding for Arteriovenous Malformation AVM is essential for medical billing, insurance authorization for specialized imaging, and tracking clinical outcomes. Because an Arteriovenous Malformation AVM involves an abnormal tangle of blood vessels connecting arteries and veins, which bypasses the capillary system, clinicians must often specify the site to ensure appropriate diagnostic protocols and surgical planning.



How are Arteriovenous Malformation AVM cases categorized?


Medical coding systems categorize Arteriovenous Malformation AVM based on both the nature of the vessel anomaly and its location within the body. Common classifications include:



  • Q27.3: Peripheral arteriovenous malformation.

  • Q28.2: Arteriovenous malformation of the cerebral vessels.

  • Q25.79: Other congenital malformations of the pulmonary vessels.

  • I77.0: Acquired arteriovenous fistula (distinct from congenital AVM).



Is Arteriovenous Malformation AVM considered a rare condition?


Yes, while Arteriovenous Malformation AVM is a complex vascular condition, it is classified as rare. At DiseaseMaps.org, we currently support a community of 200 people with Arteriovenous Malformation AVM who share their lived experiences and clinical journeys. This shared data helps researchers understand the real-world impact of living with an Arteriovenous Malformation AVM, beyond the clinical codes used in hospital records.



Next steps



  • Consult with a neurosurgeon or vascular specialist to confirm your specific ICD-10 code based on your imaging results.

  • Join the 200 members of the DiseaseMaps.org community to connect with others managing an Arteriovenous Malformation AVM.

  • Request a copy of your radiology reports to ensure your medical records accurately reflect the anatomical location of your AVM.



Medical disclaimer: This content is for informational purposes only and does not constitute professional medical advice, diagnosis, or treatment; always seek the advice of your physician regarding a medical condition.



References



  • NIH Genetic and Rare Diseases Information Center (GARD)

  • Orphanet: Portal for rare diseases and orphan drugs

  • ICD-10 Data: International Classification of Diseases, Tenth Revision

  • OMIM (Online Mendelian Inheritance in Man)

Author: DiseaseMaps Editorial Team
Reviewed against authoritative medical sources (NIH GARD, Orphanet, OMIM)
Last updated: 2026-05-08
Sources cited: NIH Genetic and Rare Diseases Information Center (GARD) · Orphanet: Portal for rare diseases and orphan drugs · ICD-10 Data: International Classification of Diseases, Tenth Revision · OMIM (Online Mendelian Inheritance in Man) · WHO
Medical disclaimer: This information does not substitute professional medical advice. Always consult your doctor before making health decisions.
Source: DiseaseMaps.org
5 answers
I would not have the faintest idea. Your doctor or his office would know this.

Posted Sep 13, 2017 by Jill 2000
There are different ICD9 and ICD10 codes for AVM in different parts of the body. Your doctor will choose the appropriate code based on your age and where your malformation is located.


Posted Nov 3, 2017 by Rhonda 2150
Probably no code, this is a rare condition, not a common one

Posted Jul 5, 2020 by Mary 2500
I have no idea what these codes refer to. Explain please

Posted Nov 3, 2022 by Heather 5020

ICD9 and ICD10 codes of Arteriovenous Malformation AVM

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