Short answer · Medically reviewed summary · Last updated: 2023-07-10
Autoimmune Lymphoproliferative Syndrome (ALPS) is a rare genetic disorder characterized by abnormal immune cell function, leading to the accumulation of lymphocytes in various organs. The ICD10 code for ALPS is D89.89, which falls under the category of "Other specified disorders involving the immune mechanism, not elsewhere classified." This code is used to classify diseases that do not have a specific code assigned. In contrast, the ICD9 code for ALPS is 279.4.
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ICD10 code of Autoimmune Lymphoproliferative Syndrome and ICD9 code
ICD-10 and ICD-9 codes for Autoimmune Lymphoproliferative Syndrome, with classification details for clinicians, coders and patients.
Autoimmune Lymphoproliferative Syndrome (ALPS) is a rare genetic disorder characterized by abnormal immune cell function, leading to the accumulation of lymphocytes in various organs. The ICD10 code for ALPS is D89.89, which falls under the category of "Other specified disorders involving the immune mechanism, not elsewhere classified." This code is used to classify diseases that do not have a specific code assigned.
In contrast, the ICD9 code for ALPS is 279.4. In the ICD9 coding system, this code is used for "Autoimmune disease, not elsewhere classified." While this code does not specifically mention ALPS, it is the closest code available in the ICD9 system to classify this disorder.
ALPS is characterized by an array of symptoms, including lymphadenopathy (enlarged lymph nodes), hepatosplenomegaly (enlarged liver and spleen), autoimmune cytopenias (low blood cell counts), and an increased risk of developing lymphoma. It is important to note that ALPS is a complex disorder, and accurate diagnosis requires a thorough evaluation by a healthcare professional, including genetic testing and specialized laboratory tests.
Treatment for ALPS typically involves managing the symptoms and complications associated with the disorder. This may include immunosuppressive medications, such as corticosteroids, to control autoimmune manifestations, as well as regular monitoring for the development of lymphomas. Additionally, supportive care measures, such as blood transfusions or splenectomy, may be necessary depending on the individual's specific symptoms and disease progression.
In contrast, the ICD9 code for ALPS is 279.4. In the ICD9 coding system, this code is used for "Autoimmune disease, not elsewhere classified." While this code does not specifically mention ALPS, it is the closest code available in the ICD9 system to classify this disorder.
ALPS is characterized by an array of symptoms, including lymphadenopathy (enlarged lymph nodes), hepatosplenomegaly (enlarged liver and spleen), autoimmune cytopenias (low blood cell counts), and an increased risk of developing lymphoma. It is important to note that ALPS is a complex disorder, and accurate diagnosis requires a thorough evaluation by a healthcare professional, including genetic testing and specialized laboratory tests.
Treatment for ALPS typically involves managing the symptoms and complications associated with the disorder. This may include immunosuppressive medications, such as corticosteroids, to control autoimmune manifestations, as well as regular monitoring for the development of lymphomas. Additionally, supportive care measures, such as blood transfusions or splenectomy, may be necessary depending on the individual's specific symptoms and disease progression.
Author: DiseaseMaps Editorial Team
Reviewed against authoritative medical sources (NIH GARD, Orphanet, OMIM)
Last updated: 2023-07-10
Medical disclaimer:
This information does not substitute professional medical advice. Always consult your doctor before making health decisions.
Source:
DiseaseMaps.org
