Empty Sella Syndrome synonyms

Empty Sella Syndrome is primarily known by that name, though it is sometimes referred to as Empty Sella Turcica or Arachnoidocele. These terms describe the same condition where the sella turcica, the bony structure housing the pituitary gland, appears empty or flattened on imaging because it has filled with cerebrospinal fluid.

What are the common synonyms for Empty Sella Syndrome?

While Empty Sella Syndrome is the standard clinical term used globally, you may encounter several alternative names in medical literature or older records. The condition is sometimes referred to as Primary Empty Sella when it occurs without a known underlying cause, or Secondary Empty Sella when it results from conditions like pituitary tumors, surgery, or radiation. Historical texts may occasionally use the term Intrasellar Herniation of the Subarachnoid Space.

How is Empty Sella Syndrome classified in medical systems?

Nomenclature varies slightly depending on the medical registry. In the International Classification of Diseases (ICD-10/11), Empty Sella Syndrome is categorized under pituitary disorders. Orphanet (ORPHA:3146) recognizes the condition by its standard name, while the NIH Genetic and Rare Diseases Information Center (GARD) provides comprehensive resources under the same designation. Because Empty Sella Syndrome is a radiological finding that may or may not be symptomatic, its classification often overlaps with endocrine and neurological databases.

Why are there multiple names for this condition?

The variety of names stems from the historical evolution of how physicians describe the Empty Sella Syndrome anatomy:

• Empty Sella Turcica: Refers to the anatomical location (the Turkish saddle-shaped bone).


• Arachnoidocele: Describes the herniation of the arachnoid membrane into the sella turcica.


• Primary vs. Secondary: Distinguishes whether the Empty Sella Syndrome occurred spontaneously or as a result of a specific medical intervention.

Next steps

• Consult an endocrinologist if you have received an Empty Sella Syndrome diagnosis to monitor pituitary function.


• Request a referral to a neuro-ophthalmologist if you experience vision changes, as Empty Sella Syndrome can sometimes impact the optic chiasm.


• Join our community at DiseaseMaps.org to connect with the 15+ members currently sharing their experiences with Empty Sella Syndrome.

Medical disclaimer: This content is for informational purposes only and does not constitute medical advice, diagnosis, or treatment; always seek the guidance of your physician or other qualified health provider.

References

• NIH Genetic and Rare Diseases Information Center (GARD): Empty Sella Syndrome.


• Orphanet: Rare Disease Database (ORPHA:3146).


• National Institute of Neurological Disorders and Stroke (NINDS): Empty Sella Syndrome.