Short answer · Medically reviewed summary · Last updated: 2026-05-08

Henoch-Schönlein purpura (HSP), now clinically referred to as IgA vasculitis, is classified under ICD-10 code D69.0 and was previously identified under ICD-9 code 287.0. These diagnostic codes are essential for medical billing, insurance authorization, and tracking the clinical progression of this systemic vasculitis. What is the clinical definition of Henoch-Schönlein purpura? Henoch-Schönlein purpura is a systemic small-vessel vasculitis characterized by the deposition of IgA-dominant immune complexes.

1 people with Henoch-Schönlein purpura have shared their first-person experience on this question at DiseaseMaps.

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ICD10 code of Henoch-Schönlein purpura and ICD9 code

ICD-10 and ICD-9 codes for Henoch-Schönlein purpura, with classification details for clinicians, coders and patients.

ICD9 and ICD10 codes of Henoch-Schönlein purpura

Henoch-Schönlein purpura (HSP), now clinically referred to as IgA vasculitis, is classified under ICD-10 code D69.0 and was previously identified under ICD-9 code 287.0. These diagnostic codes are essential for medical billing, insurance authorization, and tracking the clinical progression of this systemic vasculitis.



What is the clinical definition of Henoch-Schönlein purpura?


Henoch-Schönlein purpura is a systemic small-vessel vasculitis characterized by the deposition of IgA-dominant immune complexes. While the name Henoch-Schönlein purpura remains common in literature, modern clinical guidelines prefer the term IgA vasculitis to better describe the underlying pathology. Our community at DiseaseMaps.org includes 106 members who have navigated the diagnosis and management of Henoch-Schönlein purpura, highlighting the importance of standardized coding for consistent care.



How are ICD codes used for Henoch-Schönlein purpura?


Medical providers use the ICD-10-CM code D69.0 to document Henoch-Schönlein purpura in electronic health records. This classification allows specialists to track specific complications of Henoch-Schönlein purpura, such as renal involvement or gastrointestinal issues. Using the correct code ensures that patients receive appropriate insurance coverage for treatments and follow-up monitoring.



What diagnostic criteria accompany these codes?


Diagnosis of Henoch-Schönlein purpura typically involves meeting the EULAR/PRINTO/PRES criteria. Key clinical indicators that support the use of the D69.0 code include:



  • Palpable purpura (non-thrombocytopenic) as the primary clinical feature.

  • Arthritis or arthralgia occurring in the large joints.

  • Abdominal pain of acute onset.

  • Renal involvement, such as hematuria or proteinuria.

  • Biopsy findings showing IgA deposition in the small vessel walls.



Next steps



  • Consult a pediatric or adult rheumatologist to confirm your diagnosis and monitor for potential kidney involvement.

  • Ensure your medical records reflect the transition from the term Henoch-Schönlein purpura to IgA vasculitis for consistency with modern guidelines.

  • Join our community of 106 individuals at DiseaseMaps.org to share experiences and find local support.

  • Keep a symptom log to track skin rashes, joint pain, or gastrointestinal distress between appointments.



Medical disclaimer: This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment; always seek the advice of your physician regarding a medical condition.



References



  • Orphanet: IgA vasculitis (ORPHA:3198)

  • NIH GARD: IgA vasculitis (Henoch-Schönlein purpura)

  • ICD-10-CM Data: D69.0 (Allergic purpura)

  • American College of Rheumatology: Vasculitis in Children

Author: DiseaseMaps Editorial Team
Reviewed against authoritative medical sources (NIH GARD, Orphanet, OMIM)
Last updated: 2026-05-08
Sources cited: Orphanet: IgA vasculitis (ORPHA:3198) · NIH GARD: IgA vasculitis (Henoch-Schönlein purpura) · ICD-10-CM Data: D69.0 (Allergic purpura) · American College of Rheumatology: Vasculitis in Children · WHO
Medical disclaimer: This information does not substitute professional medical advice. Always consult your doctor before making health decisions.
Source: DiseaseMaps.org
2 answers
Icd 10 D69.0
Icd9 287.0

Posted Oct 5, 2019 by Amy 13500

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