Hereditary Fructose Intolerance (HFI) is a rare genetic disorder that impairs the body's ability to metabolize fructose, a type of sugar found in various fruits, vegetables, and sweeteners. The ICD-10 code for Hereditary Fructose Intolerance is E74.1. This code specifically identifies the condition and helps healthcare professionals accurately document and classify the disease for medical billing and statistical purposes.
In contrast, the ICD-9 code for Hereditary Fructose Intolerance is 271.2. However, it is important to note that as of October 1, 2015, the World Health Organization transitioned from ICD-9 to ICD-10 coding system for diagnostic purposes. Therefore, healthcare providers primarily use the ICD-10 code (E74.1) to identify and classify Hereditary Fructose Intolerance.
It's crucial for individuals with HFI to carefully manage their diet and avoid consuming fructose-containing foods and beverages to prevent potentially serious symptoms such as abdominal pain, vomiting, and low blood sugar. Early diagnosis and proper management are key to ensuring a healthy and fulfilling life for those affected by this condition.
Author: DiseaseMaps Editorial Team
Reviewed against authoritative medical sources (NIH GARD, Orphanet, OMIM)
Last updated: 2023-07-10
Medical disclaimer:
This information does not substitute professional medical advice. Always consult your doctor before making health decisions.