Hyperlipoproteinemia type III, also known as dysbetalipoproteinemia or broad beta disease, is a rare genetic disorder characterized by abnormal lipid metabolism. In this condition, there is an accumulation of chylomicrons and intermediate-density lipoproteins (IDL) due to impaired clearance by the liver, leading to elevated levels of cholesterol and triglycerides in the blood.
The ICD-10 code for hyperlipoproteinemia type III is E78.3. This code falls under the category of "Disorders of Lipoprotein Metabolism and Other Lipidemias" (E78) in the ICD-10 coding system. It specifically identifies the subtype of hyperlipoproteinemia characterized by the presence of chylomicron and IDL remnants in the blood.
In the previous ICD-9 coding system, hyperlipoproteinemia type III was classified under code 272.5. This code, titled "Other and unspecified hyperlipidemia," encompassed various types of hyperlipidemias, including type III. However, it is important to note that the ICD-9 code system has been replaced by ICD-10 since October 1, 2015, for diagnostic coding purposes.
Hyperlipoproteinemia type III is associated with an increased risk of atherosclerosis, which can lead to cardiovascular diseases such as coronary artery disease and peripheral vascular disease. Prompt diagnosis and appropriate management, including lifestyle modifications and lipid-lowering medications, are crucial in preventing or managing complications associated with this condition.
It is always recommended to consult with a healthcare professional or medical coder for accurate coding and diagnosis information as they can provide the most up-to-date and context-specific guidance.
Author: DiseaseMaps Editorial Team
Reviewed against authoritative medical sources (NIH GARD, Orphanet, OMIM)
Last updated: 2023-07-10
Medical disclaimer:
This information does not substitute professional medical advice. Always consult your doctor before making health decisions.