ICD10 code of Keratoconus and ICD9 code

The primary medical billing code for Keratoconus under the ICD-10-CM classification system is H18.6, while under the older ICD-9-CM system, it was coded as 371.6. These codes are used by healthcare providers to document the progressive thinning and cone-shaped protrusion of the cornea, which is the hallmark of the condition.

What is the clinical classification of Keratoconus?

Keratoconus is a non-inflammatory eye condition where the normally round, dome-shaped cornea progressively thins and begins to bulge into a cone-like shape. This structural change causes significant light refraction errors, leading to distorted vision, increased sensitivity to light, and frequent changes in eyeglass prescriptions. In the DiseaseMaps.org community, 724 people with Keratoconus have shared their experiences, highlighting how these visual challenges can impact daily tasks like driving, reading, and working.

How are ICD codes utilized for Keratoconus?

ICD (International Classification of Diseases) codes are essential for standardizing medical records and insurance billing globally. For Keratoconus, clinicians use specific sub-codes to indicate which eye is affected and the stage of the disease:

• ICD-10-CM H18.60: Keratoconus, unspecified.


• ICD-10-CM H18.61: Keratoconus, stable.


• ICD-10-CM H18.62: Keratoconus, unstable (often requiring intervention like corneal cross-linking).


• ICD-9-CM 371.60: Keratoconus, unspecified (historical code).

Is Keratoconus considered a genetic condition?

While the exact cause of Keratoconus remains a subject of intense research, data suggests a multifactorial origin involving both genetic and environmental factors. Approximately 10% to 15% of individuals with Keratoconus have a family history of the disease, suggesting a hereditary component. However, the majority of cases appear sporadically. Environmental triggers, such as chronic eye rubbing and allergic conjunctivitis, are strongly linked to the progression of corneal thinning in predisposed individuals.

How is the diagnosis and progression of Keratoconus managed?

Early diagnosis is critical for managing Keratoconus effectively. Ophthalmologists typically use corneal topography, a specialized imaging test that creates a detailed map of the corneal surface, to detect early signs of steepening. Management strategies have evolved significantly over the last decade. While early stages may be managed with rigid gas-permeable contact lenses or scleral lenses, modern treatments like corneal collagen cross-linking (CXL) are now available to stabilize the cornea and potentially halt the progression of Keratoconus, reducing the long-term need for corneal transplants.

Next steps

• Schedule a comprehensive eye examination with a cornea specialist or an optometrist experienced in managing irregular astigmatism.


• Avoid rubbing your eyes, as this mechanical stress can exacerbate the thinning of the corneal tissue.


• Connect with the 724 members on DiseaseMaps.org to share experiences and learn about coping strategies for living with vision changes.


• Inquire with your ophthalmologist about whether you are a candidate for corneal cross-linking if your condition shows signs of progression.

Medical disclaimer: This content is for informational purposes only and does not constitute professional medical advice, diagnosis, or treatment; always consult with your physician regarding your specific health needs.

References

• Orphanet (ORPHA:484): Keratoconus.


• NIH Genetic and Rare Diseases Information Center (GARD): Keratoconus.


• OMIM (Online Mendelian Inheritance in Man): Entry #148300 (Keratoconus).


• National Keratoconus Foundation (NKCF): Understanding the disease.