Short answer · Medically reviewed summary · Last updated: 2026-05-08
Paroxysmal Kinesigenic Choreathetosis (PKC), also known as Paroxysmal Kinesigenic Dyskinesia (PKD), does not have a unique, dedicated ICD-10 or ICD-9 code. Clinicians typically use the ICD-10 code G25.0 (Drug-induced subacute dyskinesia) or G25.89 (Other specified extrapyramidal and movement disorders), while ICD-9-CM utilized 333.89 (Other specified extrapyramidal disease and abnormal movement disorders) for coding this condition. Why is there no specific ICD code for Paroxysmal Kinesigenic Choreathetosis? Because Paroxysmal Kinesigenic Choreathetosis is a rare movement disorder, it is often grouped under broader categories of "extrapyramidal and movement disorders" in international billing systems.
ICD10 code of Paroxysmal Kinesigenic Choreathetosis / Dyskinesia and ICD9 code
ICD-10 and ICD-9 codes for Paroxysmal Kinesigenic Choreathetosis / Dyskinesia, with classification details for clinicians, coders and patients.
Paroxysmal Kinesigenic Choreathetosis (PKC), also known as Paroxysmal Kinesigenic Dyskinesia (PKD), does not have a unique, dedicated ICD-10 or ICD-9 code. Clinicians typically use the ICD-10 code G25.0 (Drug-induced subacute dyskinesia) or G25.89 (Other specified extrapyramidal and movement disorders), while ICD-9-CM utilized 333.89 (Other specified extrapyramidal disease and abnormal movement disorders) for coding this condition.
Why is there no specific ICD code for Paroxysmal Kinesigenic Choreathetosis?
Because Paroxysmal Kinesigenic Choreathetosis is a rare movement disorder, it is often grouped under broader categories of "extrapyramidal and movement disorders" in international billing systems. This lack of a specific code can sometimes make insurance billing or tracking of Paroxysmal Kinesigenic Dyskinesia patients challenging, as practitioners must rely on descriptive codes that encompass various involuntary movement syndromes.
What are the primary features of Paroxysmal Kinesigenic Choreathetosis?
Paroxysmal Kinesigenic Dyskinesia is characterized by brief, sudden attacks of involuntary movements triggered by a sudden change in activity or movement. Symptoms typically include:
- Dystonic posturing or choreoathetoid movements lasting less than one minute.
- Onset typically occurring in childhood or adolescence (usually between ages 5 and 15).
- High frequency of attacks, sometimes occurring dozens of times per day.
- Clear triggers such as standing up quickly, starting to run, or sudden emotional startle.
- Excellent response to low-dose anticonvulsants like carbamazepine or oxcarbazepine.
Is Paroxysmal Kinesigenic Dyskinesia hereditary?
In many cases, Paroxysmal Kinesigenic Choreathetosis is an inherited condition. Approximately 50% of familial cases are linked to mutations in the PRRT2 gene, which follows an autosomal dominant inheritance pattern. Understanding the genetic basis of Paroxysmal Kinesigenic Dyskinesia is vital for accurate diagnosis and family planning.
Next steps
- Consult a movement disorder neurologist to confirm a clinical diagnosis of Paroxysmal Kinesigenic Choreathetosis.
- Consider genetic testing for the PRRT2 gene mutation to confirm the diagnosis.
- Join the DiseaseMaps.org community to connect with the 7 other members currently living with this condition.
- Maintain a symptom diary to help your physician optimize your anticonvulsant dosage.
Medical disclaimer: This information is for educational purposes only and does not replace professional medical advice, diagnosis, or treatment.
References
- NIH Genetic and Rare Diseases Information Center (GARD): Paroxysmal Kinesigenic Dyskinesia.
- Orphanet: Paroxysmal Kinesigenic Dyskinesia (ORPHA: 247608).
- OMIM (Online Mendelian Inheritance in Man): Dyskinesia, Familial Kinesigenic, 1 (Entry #128200).
- International Parkinson and Movement Disorder Society (MDS) clinical guidelines.
