Short answer · Medically reviewed summary · Last updated: 2026-05-08

Rheumatic Fever is classified under ICD-10 code I00 (Rheumatic fever without mention of heart involvement) and various codes under I01 (Rheumatic fever with heart involvement), while under the older ICD-9 system, it was primarily categorized as 390–392. These classification codes are essential for healthcare providers to document the inflammatory response that follows a Group A streptococcal infection. What is the clinical significance of Rheumatic Fever classification? Rheumatic Fever is an autoimmune response that can occur after an untreated or inadequately treated streptococcal pharyngitis.

1 people with Rheumatic Fever have shared their first-person experience on this question at DiseaseMaps.

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ICD10 code of Rheumatic Fever and ICD9 code

ICD-10 and ICD-9 codes for Rheumatic Fever, with classification details for clinicians, coders and patients.

ICD9 and ICD10 codes of Rheumatic Fever

Rheumatic Fever is classified under ICD-10 code I00 (Rheumatic fever without mention of heart involvement) and various codes under I01 (Rheumatic fever with heart involvement), while under the older ICD-9 system, it was primarily categorized as 390–392. These classification codes are essential for healthcare providers to document the inflammatory response that follows a Group A streptococcal infection.



What is the clinical significance of Rheumatic Fever classification?


Rheumatic Fever is an autoimmune response that can occur after an untreated or inadequately treated streptococcal pharyngitis. By using specific ICD-10 and ICD-9 codes, clinicians track the systemic impact of Rheumatic Fever, which can affect the heart, joints, skin, and central nervous system. Accurate coding is critical for long-term monitoring, as patients with a history of Rheumatic Fever may require secondary antibiotic prophylaxis to prevent recurrence.



How is Rheumatic Fever diagnosed?


Diagnosis relies on the modified Jones Criteria, which categorize symptoms into major and minor manifestations. Because Rheumatic Fever often presents with varied symptoms, clinicians look for the following diagnostic indicators:



  • Carditis (inflammation of the heart)

  • Polyarthritis (migratory joint inflammation)

  • Sydenham’s chorea (involuntary, jerky movements)

  • Erythema marginatum (a specific type of rash)

  • Subcutaneous nodules



Is Rheumatic Fever hereditary?


Rheumatic Fever is not directly hereditary; however, there is a recognized genetic predisposition that influences how an individual’s immune system responds to streptococcal bacteria. While Rheumatic Fever is triggered by environmental exposure to the bacteria, family history may be discussed with a genetic counselor to understand an individual's unique susceptibility profile.



Community and support for Rheumatic Fever


Living with the aftermath of Rheumatic Fever can be overwhelming. At DiseaseMaps.org, we currently have 11 community members who share their experiences with Rheumatic Fever. Connecting with others can provide emotional support and practical strategies for managing long-term heart health and prophylactic treatment regimens.



Next steps



  • Consult a pediatric cardiologist or rheumatologist to establish a long-term care plan.

  • Ensure all streptococcal infections are treated promptly with appropriate antibiotics.

  • Join the Rheumatic Fever community at DiseaseMaps.org to share experiences with peers.

  • Discuss secondary prophylaxis duration with your physician based on the latest clinical guidelines.



Medical disclaimer: This information is for educational purposes only and does not replace professional medical advice, diagnosis, or treatment.



References



  • NIH Genetic and Rare Diseases Information Center (GARD): Rheumatic Fever overview.

  • World Health Organization (WHO): Guidelines for the prevention of Rheumatic Fever.

  • Centers for Disease Control and Prevention (CDC): Streptococcal infections and secondary prevention.

  • PubMed/NCBI: Clinical diagnostic criteria for Rheumatic Fever (Jones Criteria).

Medical disclaimer: This information does not substitute professional medical advice. Always consult your doctor before making health decisions.
Source: DiseaseMaps.org
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M06.9 Artritis reumatoide

Posted Aug 1, 2017 by MelanieMolina 2050

ICD9 and ICD10 codes of Rheumatic Fever

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