ICD10 code of Superior Mesenteric Artery Syndrome and ICD9 code

Superior Mesenteric Artery Syndrome (SMAS) is classified under the ICD-10-CM code K31.6, which covers "other diseases of the stomach and duodenum," specifically including vascular compression of the duodenum. In the older ICD-9-CM coding system, Superior Mesenteric Artery Syndrome was typically categorized under 537.89, representing other specified disorders of the stomach and duodenum.

What is Superior Mesenteric Artery Syndrome?

Superior Mesenteric Artery Syndrome is a rare digestive disorder that occurs when the third portion of the duodenum is compressed between the abdominal aorta and the overlying superior mesenteric artery. This compression happens when the mesenteric fat pad, which normally cushions the duodenum, is depleted. Our community at DiseaseMaps.org currently supports 380 people living with Superior Mesenteric Artery Syndrome, highlighting the importance of shared experiences in navigating this complex condition.

How is Superior Mesenteric Artery Syndrome diagnosed?

Diagnosis of Superior Mesenteric Artery Syndrome often requires advanced imaging to visualize the narrowed aortomesenteric angle. Clinicians typically look for the following diagnostic markers:

• Aortomesenteric angle: A reduction of the angle between the aorta and the superior mesenteric artery to less than 22–28 degrees.


• Aortomesenteric distance: A distance between these two vessels of less than 8–10 mm.


• Duodenal obstruction: Visible dilation of the proximal duodenum with a sharp cutoff at the level of the artery during imaging.

What are the primary treatment approaches for Superior Mesenteric Artery Syndrome?

Initial management for Superior Mesenteric Artery Syndrome usually focuses on conservative measures to restore the retroperitoneal fat pad. This includes nutritional rehabilitation, such as high-calorie oral supplementation or post-pyloric enteral feeding. If conservative efforts fail to resolve the symptoms of Superior Mesenteric Artery Syndrome, surgical intervention, such as a duodenojejunostomy, may be necessary to bypass the obstruction.

Next steps

• Consult with a gastroenterologist or a vascular surgeon specializing in rare anatomical compressions.


• Join the 380 members at DiseaseMaps.org to connect with others who understand the challenges of Superior Mesenteric Artery Syndrome.


• Keep a detailed food and symptom diary to share with your medical team to track progress during nutritional therapy.

Medical disclaimer: This information is for educational purposes and does not replace professional medical advice, diagnosis, or treatment from a qualified healthcare provider.

References

• National Institutes of Health (NIH) - Genetic and Rare Diseases Information Center (GARD)


• Orphanet: Portal for rare diseases and orphan drugs


• National Center for Biotechnology Information (NCBI) - PubMed Central


• DiseaseMaps.org community data resources