Short answer · Medically reviewed summary · Last updated: 2026-05-08
Dermatofibrosarcoma protuberans (DFSP) is classified under the ICD-10-CM code C44.91 (Malignant neoplasm of skin of unspecified site, specifically for dermatofibrosarcoma protuberans) or more broadly under code C44 depending on the anatomical location. Under the older ICD-9-CM classification system, dermatofibrosarcoma protuberans (DFSP) was identified by code 173.9. What is the clinical classification of Dermatofibrosarcoma Protuberans? Dermatofibrosarcoma protuberans (DFSP) is a rare, slow-growing, locally aggressive soft tissue sarcoma that originates in the dermis.
2 people with Dermatofibrosarcoma Protuberans (DFSP) have shared their first-person experience on this question at DiseaseMaps.
ICD10 code of Dermatofibrosarcoma Protuberans (DFSP) and ICD9 code
ICD-10 and ICD-9 codes for Dermatofibrosarcoma Protuberans (DFSP), with classification details for clinicians, coders and patients.
Dermatofibrosarcoma protuberans (DFSP) is classified under the ICD-10-CM code C44.91 (Malignant neoplasm of skin of unspecified site, specifically for dermatofibrosarcoma protuberans) or more broadly under code C44 depending on the anatomical location. Under the older ICD-9-CM classification system, dermatofibrosarcoma protuberans (DFSP) was identified by code 173.9.
What is the clinical classification of Dermatofibrosarcoma Protuberans?
Dermatofibrosarcoma protuberans (DFSP) is a rare, slow-growing, locally aggressive soft tissue sarcoma that originates in the dermis. Because dermatofibrosarcoma protuberans (DFSP) has a high risk of local recurrence but a low risk of distant metastasis, medical coding is essential for tracking treatment outcomes and insurance coverage for excision surgeries, which remain the gold standard of care.
How are ICD codes used for Dermatofibrosarcoma Protuberans (DFSP)?
Accurate coding for dermatofibrosarcoma protuberans (DFSP) is vital for coordinating multidisciplinary care, including dermatology, surgical oncology, and pathology. When your provider submits billing, they must specify the anatomical site to ensure the correct ICD-10 code is applied. Common sites for dermatofibrosarcoma protuberans (DFSP) include the trunk and proximal extremities.
What should patients know about the diagnostic journey?
Receiving a diagnosis of dermatofibrosarcoma protuberans (DFSP) can be overwhelming. Understanding the administrative side of your condition, such as diagnostic coding, is one way to feel more empowered during your clinical visits. Our community at DiseaseMaps.org currently includes 172 members who have navigated these systems and shared their experiences with dermatofibrosarcoma protuberans (DFSP).
- ICD-10 Code: C44.91 (or site-specific C44.x codes)
- ICD-9 Code: 173.9
- Pathology: Often characterized by the t(17;22) translocation involving the COL1A1-PDGFB fusion gene.
Next steps
- Consult with a surgical oncologist or a Mohs surgeon experienced in treating dermatofibrosarcoma protuberans (DFSP).
- Request a copy of your pathology report to confirm the exact diagnosis and margin status.
- Join the 172 members on DiseaseMaps.org to connect with others who understand the diagnostic and treatment path.
- Discuss long-term surveillance plans with your care team, as local recurrence can occur years after initial treatment.
Medical disclaimer: This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment; always seek the advice of your physician or other qualified health provider with any questions regarding a medical condition.
References
- NIH Genetic and Rare Diseases Information Center (GARD): Dermatofibrosarcoma protuberans
- Orphanet: Dermatofibrosarcoma protuberans (ORPHA:227)
- National Cancer Institute (NCI) Physician Data Query (PDQ): Soft Tissue Sarcoma Treatment
- OMIM (Online Mendelian Inheritance in Man): Dermatofibrosarcoma protuberans (#607172)
Posted Sep 11, 2017 by Kelly 2100
Posted Sep 12, 2017 by Deana 2000
